hội chứng thực bào máu liên quan đến nhiễm trùng ở bệnh nhân người lớn tại bệnh viện bệnh nhiệt đới

cytosis with rituximab-containing chemo-immunotherapeutic
regimens", British Journal of Haematology, 162(3), pp.376-382.
41. Chen J, Wang X, He P, Li Y, Si M, Fan Z, et al. (2015), "Viral etiology, clinical
and laboratory features of adult hemophagocytic lymphohistiocytosis",
Journal of medical virology, 88(3), pp.541-549.


42. Chuang HC, Lay JD, Hsieh WC, Wang HC, Chang Y, Chuang SE, et al. (2005),
"Epstein-Barr virus LMP1 inhibits the expression of SAP gene and
upregulates Th1 cytokines in the pathogenesis of hemophagocytic
syndrome", Blood, 106(9), pp.3090-3096.
43. De-Lavaissiere M, Manceron V, Bouree P, Garcon L, Bisaro F, Delfraissy JF, et
al. (2009), "Reconstitution inflammatory syndrome related to histoplasmosis,
with a hemophagocytic syndrome in HIV infection", The Journal of
infection, 58(3), pp.245-247.
44. Deane S, Selmi C, Teuber SS, Gershwin ME (2010), "Macrophage activation
syndrome in autoimmune disease", International archives of allergy and
immunology, 153(2), pp.109-120.
45. Doyle T, Bhagani S, Cwynarski K (2009), "Haemophagocytic syndrome and
HIV", Current opinion in infectious diseases, 22(1), pp.1-6.
46. den Dunnen JT, Antonarakis SE (2000), "Mutation nomenclature extensions and
suggestions to describe complex mutations: a discussion", Human mutation,
15(1), pp.7-12.
47. Emmenegger U., Spaeth P. J., Neftel K. A. (2002), "Intravenous
immunoglobulin for hemophagocytic lymphohistiocytosis?", Journal of
clinical oncology: official journal of the American Society of Clinical
Oncology, 20(2), 599-601.
48. Farquhar JW, Claireaux AE (1952), "Familial haemophagocytic reticulosis",
Archives of disease in childhood, 27(136), pp.519-525.
49. Feldmann J, Callebaut I, Raposo G, Certain S, Bacq D, Dumont C, et al. (2003),
"Munc13-4 is essential for cytolytic granules fusion and is mutated in a form

of familial hemophagocytic lymphohistiocytosis (FHL3)", Cell, 115(4),
pp.461-473.
50. Filipovich A, McClain K, Grom A (2010), "Histiocytic disorders: recent
insights into pathophysiology and practical guidelines", Biology of blood and
marrow transplantation: journal of the American Society for Blood and
Marrow Transplantation, 16(1 Suppl), S82-89.
51. George MR (2014), "Hemophagocytic lymphohistiocytosis: review of etiologies
and management", Journal of blood medicine, 5(1), pp.69-86.
52. Gholam C, Grigoriadou S, Gilmour KC, Gaspar HB (2011), "Familial
haemophagocytic lymphohistiocytosis: advances in the genetic basis,
diagnosis and management", Clinical and experimental immunology, 163(3),
pp.271-283.


53. Grom AA (2004), "Natural killer cell dysfunction: A common pathway in
systemic-onset juvenile rheumatoid arthritis, macrophage activation
syndrome, and hemophagocytic lymphohistiocytosis?", Arthritis and
rheumatism, 50(3), pp.689-698.
54. Gupta A, Tyrrell P, Valani R, Benseler S, Weitzman S, Abdelhaleem M (2008),
"The role of the initial bone marrow aspirate in the diagnosis of
hemophagocytic lymphohistiocytosis", Pediatric blood & cancer, 51(3),
pp.402-404.
55. Hardikar W, Pang K, Al-Hebbi H, Curtis N, Couper R (2006), "Successful
treatment of cytomegalovirus associated haemophagocytic syndrome
following paediatric orthotopic liver transplantation", J Paediatr Child
Health, 42(6), pp.389-391.
56. Henter JI, Horne A, Aricó M, Egeler RM, Filipovich AH, Imashuku S, et al.
(2007), "HLH-2004: Diagnostic and therapeutic guidelines for
hemophagocytic lymphohistiocytosis", Pediatr Blood Cancer, 48(2), pp.124131.
57. Henter JI, Samuelsson-Horne A, Arico M (2002), "Treatment of

hemophagocytic lymphohistiocytosis with HLH-94 immunochemotherapy
and bone marrow transplantation", Blood, 100(7), pp.2367-2373.
58. Henter JI, Arico M, Egeler RM, Elinder G, Favara BE, Filipovich AH, et al.
(1997), "HLH-94: a treatment protocol for hemophagocytic
lymphohistiocytosis. HLH study Group of the Histiocyte Society", Medical
and pediatric oncology, 28(5), pp.342-347.
59. Horne A, Trottestam H, Arico M, Egeler RM, Filipovich AH, Gadner H, et al.
(2008), "Frequency and spectrum of central nervous system involvement in
193 children with haemophagocytic lymphohistiocytosis", British Journal of
Haematology, 140(3), pp.327-335.
60. Hui YM, Pillinger T, Luqmani A, Cooper N (2015), "Haemophagocytic
lymphohistiocytosis associated with Mycobacterium tuberculosis infection",
BMJ case reports, 2015, pii: bcr2014208220. doi: 10.1136/bcr-2014-208220.
61. Imashuku S (2002), "Clinical features and treatment strategies of Epstein-Barr
virus-associated hemophagocytic lymphohistiocytosis", Critical reviews in
oncology/hematology, 44(3), pp.259-272.
62. Imashuku S (2007), "Etoposide-related secondary acute myeloid leukemia (tAML) in hemophagocytic lymphohistiocytosis", Pediatric blood & cancer,
48(2), pp.121-123.
63. Imashuku S (2011), "Treatment of Epstein-Barr Virus-related Hemophagocytic
Lymphohistiocytosis (EBV-HLH); Update 2010", Journal of pediatric
hematology/oncology, 33(1), pp.35-39.


64. Imashuku S, Kuriyama K, Teramura T, Ishii E, Kinugawa N, Kato M, et al.
(2001), "Requirement for etoposide in the treatment of Epstein-Barr virusassociated hemophagocytic lymphohistiocytosis", Journal of clinical
oncology: official journal of the American Society of Clinical Oncology,
19(10), pp.2665-2673.
65. Imashuku S, Teramura T, Tauchi H, Ishida Y, Otoh Y, Sawada M, et al. (2004),
"Longitudinal follow-up of patients with Epstein-Barr virus-associated
hemophagocytic lymphohistiocytosis", Haematologica, 89(2), pp.183-188.

66. Institut Virion\Serion GmbH (2012), "SERION ELISA classic Epstein-Barr
Virus", />67. Ishii E, Ohga S, Imashuku S, Yasukawa M, Tsuda H, Miura I, et al. (2007),
"Nationwide survey of hemophagocytic lymphohistiocytosis in Japan",
International journal of hematology, 86(1), pp.58-65.
68. Ito S, Takada N, Ozasa A, Hanada M, Sugiyama M, Suzuki K, et al. (2006),
"Secondary hemophagocytic syndrome in a patient with methicillin-sensitive
Staphylococcus aureus bacteremia due to severe decubitus ulcer", Internal
medicine, 45(5), pp.303-307.
69. Jain D, Singh T (2008), "Dengue virus related hemophagocytosis: a rare case
report", Hematology, 13(5), pp.286-288.
70. Janka G (2009), "Hemophagocytic lymphohistiocytosis: when the immune
system runs amok", Klinische Padiatrie, 221(5), pp.278-285.
71. Janka GE (2012), "Familial and acquired hemophagocytic lymphohistiocytosis",
Annual review of medicine, 63, pp.233-246.
72. Jordan MB, Allen CE, Weitzman S, Filipovich AH, McClain KL (2011), "How
We
treat
hemophagocytic
lymphohistocytosis",
blood,
bloodjournal.hematologylibrary.org, 118(15), pp.4041-4052.
73. Joshi PP, Shegokar VR, Powar RM, Herder S, Katti R, Salkar HR, et al. (2005),
"Human trypanosomiasis caused by Trypanosoma evansi in India: the first
case report", The American journal of tropical medicine and hygiene, 73(3),
pp.491-495.
74. Kasahara Y, Yachie A (2002), "Cell type specific infection of Epstein-Barr
virus (EBV) in EBV-associated hemophagocytic lymphohistiocytosis and
chronic active EBV infection", Critical reviews in oncology/hematology,
44(3), pp.283-294.
75. Kelesidis T, Humphries R, Terashita D, Eshaghian S, Territo MC, Said J, et al.

(2012), "Epstein-Barr virus-associated hemophagocytic lymphohistiocytosis
in Los Angeles County.", J Med Virol, 84(5), pp.777-785.


76. van Koeveringe MP, Brouwer RE (2010), "Histoplasma capsulatum reactivation
with haemophagocytic syndrome in a patient with chronic lymphocytic
leukaemia", The Netherlands journal of medicine, 68(12), pp.418-21.
77. Lam T My, Le B Lien, Wen-Chuan Hsieh, Toshihiko Imamura, Tran NK Anh,
Phan N. L. Anh, et al. (2009), "Comprehensive analyses and characterization
of haemophagocytic lymphohistiocytosis in Vietnamese children", British
Journal of Haematology, 148(2), pp.301–310.
78. Lehmberg K, Ehl S (2013), "Diagnostic evaluation of patients with suspected
haemophagocytic lymphohistiocytosis", British Journal of Haematology,
160(3), pp.275-287.
79. Levy M. M., M. P. Fink, J. C. Marshall, E. Abraham, D. Angus, D. Cook, et al.
(2003), "2001 SCCM/ESICM/ACCP/ATS/SIS International Sepsis
Definitions Conference", Intensive care medicine, 29(4), pp.530-538.
80. Lin TF, Ferlic-Stark LL, Allen CE, Kozinetz CA, McClain KL (2011), "Rate of
decline of ferritin in patients with hemophagocytic lymphohistiocytosis as a
prognostic variable for mortality", Pediatric blood & cancer, 56(1), pp.154155.
81. Lo MM, Mo JQ, Dixon BP, Czech KA (2010), "Disseminated histoplasmosis
associated with hemophagocytic lymphohistiocytosis in kidney transplant
recipients", American journal of transplantation: official journal of the
American Society of Transplantation and the American Society of Transplant
Surgeons, 10(3), pp.687-691.
82. Meeths M, Chiang SC, Wood SM, Entesarian M, Schlums H, Bang B, et al.
(2011), "Familial hemophagocytic lymphohistiocytosis type 3 (FHL3)
caused by deep intronic mutation and inversion in UNC13D", Blood,
118(22), pp.5783-5793.
83. Menasche G, Feldmann J, Fischer A, de Saint Basile G (2005), "Primary

hemophagocytic syndromes point to a direct link between lymphocyte
cytotoxicity and homeostasis", Immunological reviews, 203, pp.165-179.
84. Mulders-Manders C., Simon A., Bleeker-Rovers C. (2015), "Fever of unknown
origin", Clinical medicine, 15(3), 280-284.
85. Nadine GR, Naasha JT, Camille V, Kelly C, Roger M, Carolyn G (2007),
"Infections associated with haemophagocytic syndrome", Lancet Infect Dis,
7(12), pp.814-822.
86. Nadine RM, Abeer M, Jesse TJ, Helmut A (2010), "Viral infections associated
with haemophagocytic syndrome", Rev. Med. Virol, 20, pp.93-105.


87. Nagafuji K, Nonami A, Kumano T, Kikushige Y, Yoshimoto G, Takenaka K, et
al. (2007), "Perforin gene mutations in adult-onset hemophagocytic
lymphohistiocytosis", Haematologica, 92(7), pp.978-981.
88. Nakamura I, Nakamura-Uchiyama F, Komiya N, Ohnishi K (2009), "[A case of
dengue fever with viral-associated hemophagocytic syndrome]",
Kansenshogaku zasshi. The Journal of the Japanese Association for
Infectious Diseases, 83(1), pp.60-63.
89. Nelson ER, Bierman HR, Chulajata R (1966), "Hematologic phagocytosis in
postmortem bone marrows of dengue hemorrhagic fever", The American
journal of the medical sciences, 252(1), pp.68-74.
90. Neşe Y, Işıl Yıldırım, Ebru Arık, Pelin Zorlu, Gönül Tanır (2010),
"Hemophagocytic Syndrome Associated with Bacterial Infections", J Pediatr
Inf, 4, pp.162-164.
91. Ohnishi K, Mitsui K, Komiya N, Iwasaki N, Akashi A, Hamabe Y (2007),
"CLINICAL case report: falciparum malaria with hemophagocytic
syndrome", Am J Trop Med Hyg, 76(6), pp.1016-1018.
92. Oloomi Z, Moayeri H (2006), "Cytomegalovirus infection-associated
hemophagocytic syndrome", Archives of Iranian medicine, 9(3), pp.284-287.
93. Oto M, Yoshitsugu K, Uneda S, Nagamine M, Yoshida M (2015), "Prognostic

Factors
and
Outcomes
of
Adult-Onset
Hemophagocytic
Lymphohistiocytosis: A Retrospective Analysis of 34 Cases", Hematology
reports, 7(5841), pp.48-51.
94. Pandey M, Dhingra B, Sharma S, Chandra J, Pemde H, Singh V (2012),
"Enteric
Fever
presenting
as
secondary
hemophagocytic
lymphohistiocytosis", Indian journal of pediatrics, 79(12), pp.1671-1672.
95. Parikh SA, Kapoor P, Letendre L, Kumar S, Wolanskyj AP (2014), "Prognostic
factors and outcomes of adults with hemophagocytic lymphohistiocytosis",
Mayo Clinic proceedings, 89(4), pp.484-492.
96. Park KH, Yu HS, Jung SI, Shin DH, Shin JH (2008), "Acute human
immunodeficiency virus syndrome presenting with hemophagocytic
lymphohistiocytosis", Yonsei medical journal, 49(2), pp.325-328.
97. Ramachandran B, Balasubramanian S, Abhishek N, Ravikumar KG, Ramanan
AV (2011), "Profile of hemophagocytic lymphohistiocytosis in children in a
tertiary care hospital in India", Indian pediatrics, 48(1), pp.31-35.
98. Ramanathan M, Duraisamy G (1991), "Haemophagocytosis in dengue
haemorrhagic fever: a case report", Annals of the Academy of Medicine,
Singapore, 20(6), pp.803-804.

99. Ramos-Casals M, Brito-Zeron P, Lopez-Guillermo A, Khamashta MA, Bosch X
(2014), "Adult haemophagocytic syndrome", Lancet, 383(9927), pp.15031516.
100. Raschke RA, Garcia-Orr R (2011), "Hemophagocytic lymphohistiocytosis: a
potentially underrecognized association with systemic inflammatory
response syndrome, severe sepsis, and septic shock in adults", Chest, 140(4),
pp.933-938.
101. Ray S, Kundu S, Saha M, Chakrabarti P (2011), "Hemophagocytic syndrome
in classic dengue Fever", Journal of global infectious diseases, 3(4), pp.399401.
102. Risdall RJ, Brunning RD, Hernandez JI, Gordon DH (1984), "Bacteriaassociated hemophagocytic syndrome", Cancer, 54(12), pp.2968-2972.
103. Risdall RJ, McKenna RW, Nesbit ME, Krivit W, Balfour HH Jr, Simmons RL,
et al. (1979), "Virus-associated hemophagocytic syndrome: a benign
histiocytic proliferation distinct from malignant histiocytosis", Cancer,
44(3), pp.993-1002.
104. Riviere S, Galicier L, Coppo P, Marzac C, Aumont C, Lambotte O, et al.
(2014), "Reactive hemophagocytic syndrome in adults: a retrospective
analysis of 162 patients", The American journal of medicine, 127(11),
pp.1118-1125.
105. Rosado FG, Kim AS (2013), "Hemophagocytic lymphohistiocytosis: an update
on diagnosis and pathogenesis", American journal of clinical pathology,
139(6), pp.713-727.
106. Roth AR, Basello GM (2003), "Approach to the adult patient with fever of
unknown origin", American family physician, 68(11), pp.2223-2228.
107. Rueda E, Mendez A, Gonzalez G (2002), "[Hemophagocytic syndrome
associated with dengue hemorrhagic fever]", Biomedica: revista del Instituto
Nacional de Salud, Sindrome hemofagocitico asociado con dengue
hemorragico., 22(2), pp.160-166.
108. Santos JA, Neves JF, Venancio P, Gouveia C, Varandas L (2015),
"Hemophagocytic lymphohistiocytosis secondary to Falciparum malaria in a
5 year-old boy", Annals of hematology, 94(1), pp.161-163.
109. Scott Rb, Robb-Smith Aht (1939), "Histiocytic medullary reticulosis", Lancet,

2, pp.194-198.
110. Schneider EM, Lorenz I, Muller-Rosenberger M, Steinbach G, Kron M, JankaSchaub GE (2002), "Hemophagocytic lymphohistiocytosis is associated with
deficiencies of cellular cytolysis but normal expression of transcripts relevant
to killer-cell-induced apoptosis", Blood, 100(8), pp.2891-2898.


111. Schram AM, Campigotto F, Mullally A, Fogerty A, Massarotti E, Neuberg D,
et al. (2015), "Marked hyperferritinemia does not predict for HLH in the
adult population", Blood, 125(10), pp.1548-1552.
112.

Schram AM, Berliner N (2015), "How I treat hemophagocytic
lymphohistiocytosis in the adult patient", Blood, 125(19), pp.2908-2914.

113. Schram AM, Comstock P, Campo M, Gorovets D, Mullally A, Bodio K, et al.
(2016), "Haemophagocytic lymphohistiocytosis in adults: a multicentre case
series over 7 years", British Journal of Haematology, 172(3), pp.412-419.
114. Sieni E, Cetica V, Santoro A, Beutel K, Mastrodicasa E, Meeths M, et al.
(2011), "Genotype-phenotype study of familial haemophagocytic
lymphohistiocytosis type 3", Journal of medical genetics, 48(5), pp.343-352.
115. Silva Aleksandro Schafer da, et al (2009), "Trypanosoma evansi susceptibility
to amphotericin B", Cienc. Rural [online], 39(9), pp. 2550-2555.
116. Singer M, Deutschman CS, Seymour CW, Shankar-Hari M, Annane D, Bauer
M, et al. (2016), "The Third International Consensus Definitions for Sepsis
and Septic Shock (Sepsis-3)", JAMA, 315(8), pp.801-810.
117. Singh ZN, Rakheja D, Yadav TP, Shome DK (2005), "Infection-associated
haemophagocytosis: the tropical spectrum", Clinical and laboratory
haematology, 27(5), pp.312-315.
118. Sonavane AD, Sonawane PB, Chandak SV, Rathi PM (2016), "Disseminated
Histoplasmosis with Haemophagocytic Lymphohistiocytosis in an

Immunocompetent Host", Journal of clinical and diagnostic research:
JCDR, 10(3), OD03-5.
119. Sonke GS, Ludwig I, van Oosten H, Baars JW, Meijer E, Kater AP, et al.
(2008), "Poor outcomes of chronic active Epstein-Barr virus infection and
hemophagocytic lymphohistiocytosis in non-Japanese adult patients",
Clinical infectious diseases: an official publication of the Infectious Diseases
Society of America, 47(1), pp.105-108.
120.

Srichaikul T, Punyagupta S, Kanchanapoom T, Chanokovat C,
Likittanasombat K, Leelasiri A (2008), "Hemophagocytic syndrome in
Dengue hemorrhagic fever with severe multiorgan complications", Journal
of the Medical Association of Thailand = Chotmaihet thangphaet, 91(1),
pp.104-109.

121. zur Stadt U, Rohr J, Seifert W, Koch F, Grieve S, Pagel J, et al. (2009),
"Familial hemophagocytic lymphohistiocytosis type 5 (FHL-5) is caused by
mutations in Munc18-2 and impaired binding to syntaxin 11", American
journal of human genetics, 85(4), pp.482-492.


122. Zur Stadt U, Beutel K, Kolberg S (2006), "Mutation spectrum in children with
primary hemophagocytic lymphohistiocytosis: molecular and functional
analyses of PRF1, UNC13D, STX11, and RAB27A", Hum Mutat, 27, pp.6268.
123. zur Stadt U, Schmidt S, Kasper B, Beutel K, Diler AS, Henter JI, et al. (2005),
"Linkage of familial hemophagocytic lymphohistiocytosis (FHL) type-4 to
chromosome 6q24 and identification of mutations in syntaxin 11", Human
molecular genetics, 14(6), pp.827-834.
124. Stepp SE, Dufourcq-Lagelouse R, Le Deist F, Bhawan S, Certain S, Mathew
PA, et al. (1999), "Perforin gene defects in familial hemophagocytic

lymphohistiocytosis", Science, 286(5446), pp.1957-1959.
125. Sullivan J. L., Woda B. A., Herrod H. G., Koh G., Rivara F. P., Mulder C.
(1985), "Epstein-Barr virus-associated hemophagocytic syndrome:
virological and immunopathological studies", Blood, 65(5), pp.1097-1104.
126. Sun HY, Chen MY, Fang CT, Hsieh SM, Hung CC, Chang SC (2004),
"Hemophagocytic lymphohistiocytosis: an unusual initial presentation of
acute HIV infection", Journal of acquired immune deficiency syndromes,
37(4), pp.1539-1540.
127. Sung PS, Kim IH, Lee JH, Park JW (2011), "Hemophagocytic
Lymphohistiocytosis (HLH) Associated with Plasmodium vivax Infection:
Case Report and Review of the Literature", Chonnam Med J, 47(3), pp.173176.
128. Tan LH, Lum LC, Omar SF, Kan FK (2012), "Hemophagocytosis in dengue:
comprehensive report of six cases", Journal of clinical virology: the official
publication of the Pan American Society for Clinical Virology, 55(1), pp.7982.
129. Teramura T, Tabata Y, Yagi T, Morimoto A, Hibi S, Imashuku S (2002),
"Quantitative analysis of cell-free Epstein-Barr virus genome copy number
in patients with EBV-associated hemophagocytic lymphohistiocytosis",
Leukemia & lymphoma, 43(1), pp.173-179.
130. Townsend JL, Shanbhag S, Hancock J, Bowman K, Nijhawan AE (2015),
"Histoplasmosis-Induced Hemophagocytic Syndrome: A Case Series and
Review of the Literature", Open forum infectious diseases, 2(2), ofv055.
131. Tseng YT, Sheng WH, Lin BH, Lin CW, Wang JT, Chen YC, et al. (2011),
"Causes, clinical symptoms, and outcomes of infectious diseases associated
with hemophagocytic lymphohistiocytosis in Taiwanese adults", Journal of
microbiology, immunology, and infection = Wei mian yu gan ran za zhi,
44(3), pp.191-197.


132. Trizzino A, zur Stadt U, Ueda I, Risma K, Janka G, Ishii E, et al. (2008),
"Genotype-phenotype

study
of
familial
haemophagocytic
lymphohistiocytosis due to perforin mutations", Journal of medical genetics,
45(1), pp.15-21.
133. Trottestam H, Horne A, Arico M, Egeler RM, Filipovich AH, Gadner H, et al.
(2011), "Chemoimmunotherapy for hemophagocytic lymphohistiocytosis:
long-term results of the HLH-94 treatment protocol", Blood, 118(17),
pp.4577-4584.
134. Truc P, Buscher P, Cuny G, Gonzatti MI, Jannin J, Joshi P, et al. (2013),
"Atypical human infections by animal trypanosomes", PLoS neglected
tropical diseases, 7(9), e2256.
135. Ueda I, Morimoto A, Inaba T, Yagi T, Hibi S, Sugimoto T, et al. (2003),
"Characteristic
perforin
gene
mutations
of
haemophagocytic
lymphohistiocytosis patients in Japan", British Journal of Haematology,
121(3), pp.503-510.
136. Veerakul G, Sanpakit K, Tanphaichitr VS, Mahasandana C, Jirarattanasopa N
(2002), "Secondary hemophagocytic lymphohistiocytosis in children: an
analysis of etiology and outcome", Journal of the Medical Association of
Thailand = Chotmaihet thangphaet, 85 Suppl 2, S530-541.
137. Vijayalakshmi AM, Ganesh VR (2009), "Hemophagocytic syndrome
associated with dengue hemorrhagic fever", Indian pediatrics, 46(6), pp.545.
138. Vinoth PN, Thomas KA, Selvan SM, Suman DF, Scott JX (2011),
"Hemophagocytic syndrome associated with Plasmodium falciparum

infection", Indian journal of pathology & microbiology, 54(3), pp.594-596.
139. Voskoboinik I, Sutton VR, Ciccone A, House CM, Chia J, Darcy PK, et al.
(2007), "Perforin activity and immune homeostasis: the common A91V
polymorphism in perforin results in both presynaptic and postsynaptic
defects in function", Blood, 110(4), pp.1184-1190.
140. Voves C, Wuillemin WA, Zeerleder S (2006), "International Society on
Thrombosis and Haemostasis score for overt disseminated intravascular
coagulation predicts organ dysfunction and fatality in sepsis patients", Blood
coagulation & fibrinolysis: an international journal in haemostasis and
thrombosis, 17(6), pp.445-451.
141. Wada T, Kurokawa T, Toma T, Shibata F, Tone Y, Hashida Y, et al. (2007),
"Immunophenotypic analysis of Epstein-Barr virus (EBV)-infected CD8(+)
T cells in a patient with EBV-associated hemophagocytic
lymphohistiocytosis", European journal of haematology, 79(1), pp.72-75.


142. Watanabe H, Hirase N, Goda H, Nishikawa H, Ikuyama S (2012), "Oral lowdose tacrolimus therapy for refractory hemophagocytic syndrome associated
with systemic lupus erythematosus", Modern rheumatology, 22(2), pp.284-9.
143. Weitzman S (2011), "Approach to hemophagocytic syndromes", Hematology /
the Education Program of the American Society of Hematology. American
Society of Hematology. Education Program, 2011, pp.178-83. doi:
10.1182/asheducation-2011.1.178.
144. Wheat LJ, Freifeld AG, Kleiman MB, Baddley JW, McKinsey DS, Loyd JE, et
al. (2007), "Clinical practice guidelines for the management of patients with
histoplasmosis: 2007 update by the Infectious Diseases Society of America",
Clinical infectious diseases: an official publication of the Infectious Diseases
Society of America, 45(7), pp.807-825.
145. Wong KF, Chan JK, Chan JC, Lim WW, Wong WK (1991), "Dengue virus
infection-associated hemophagocytic syndrome", American journal of
hematology, 38(4), pp.339-340.

146. World Health Organization and the Special Programme for Research and
Training in Tropical Diseases (2009), Dengue guidelines for
diagnosis,treatment, prevention and control: New edition, URL:
/>147. World Health Organization (2013), "Control and surveillance of human
African trypanosomiasis", World Health Organization technical report
series, 984, pp.1-237.
148. Yamashita N, Kimura H, Morishima T (2005), "Virological aspects of EpsteinBarr virus infections", Acta medica Okayama, 59(6), pp.239-246.
149. Yoon HS, Kim HJ, Yoo KH, Sung KW, Koo HH, Kang HJ, et al. (2010),
"UNC13D is the predominant causative gene with recurrent splicing
mutations in Korean patients with familial hemophagocytic
lymphohistiocytosis", Haematologica, 95(4), pp.622-626.
150. Zhang K, Biroschak J, Glass DN, Thompson SD, Finkel T, Passo MH, et al.
(2008), "Macrophage activation syndrome in patients with systemic juvenile
idiopathic arthritis is associated with MUNC13-4 polymorphisms", Arthritis
and rheumatism, 58(9), pp.2892-2896.
151. Zhang K, Jordan MB, Marsh RA, Johnson JA, Kissell D, Meller J, et al.
(2011), "Hypomorphic mutations in PRF1, MUNC13-4, and STXBP2 are
associated with adult-onset familial HLH", Blood, 118(22), pp.5794-5798.
152. Zhizhuo H, Junmei X, Yuelin S, Qiang Q, Chunyan L, Zhengde X, et al.
(2012), "Screening the PRF1, UNC13D, STX11, SH2D1A, XIAP, and ITK
gene mutations in Chinese children with Epstein-Barr virus-associated
hemophagocytic lymphohistiocytosis.", Pediatr Blood Cancer, 58(3),
pp.410-414.